{"id":6283,"date":"2016-09-29T09:40:12","date_gmt":"2016-09-29T08:40:12","guid":{"rendered":"http:\/\/www.fundacionisabelgemio.com\/fr\/?page_id=6283"},"modified":"2016-09-29T09:40:12","modified_gmt":"2016-09-29T08:40:12","slug":"une-biologie-une-physiopathologie-et-une-therapie-des-cellules-satellite-du-muscle-squelettique","status":"publish","type":"page","link":"https:\/\/www.fundacionisabelgemio.com\/fr\/que-faisons-nous\/une-biologie-une-physiopathologie-et-une-therapie-des-cellules-satellite-du-muscle-squelettique","title":{"rendered":"Une biologie, une physiopathologie et une th\u00e9rapie des cellules satellite du muscle squelettique"},"content":{"rendered":"\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-av_section-1410f7e6be3791a849a7730ec4d02faf\">\n.avia-section.av-av_section-1410f7e6be3791a849a7730ec4d02faf{\nbackground-repeat:no-repeat;\nbackground-image:url(https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/02\/IMG_0096_15.jpg);\nbackground-position:0% 0%;\nbackground-attachment:scroll;\n}\n.avia-section.av-av_section-1410f7e6be3791a849a7730ec4d02faf .av-section-color-overlay{\nopacity:0.7;\nbackground-color:#2e2e2e;\n}\n<\/style>\n<div id='av_section_1'  class='avia-section av-av_section-1410f7e6be3791a849a7730ec4d02faf main_color avia-section-default avia-no-shadow  avia-builder-el-0  el_before_av_layout_row  avia-builder-el-first  avia-full-stretch avia-bg-style-scroll av-section-color-overlay-active container_wrap sidebar_right'  data-section-bg-repeat='stretch'><div class=\"av-section-color-overlay-wrap\"><div class=\"av-section-color-overlay\"><\/div><div class='container av-section-cont-open' ><main  role=\"main\" itemprop=\"mainContentOfPage\"  class='template-page content  av-content-small alpha units'><div class='post-entry post-entry-type-page post-entry-6283'><div class='entry-content-wrapper clearfix'>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-av_heading-730eb818ebc425e36f3bec10155f64f7\">\n#top .av-special-heading.av-av_heading-730eb818ebc425e36f3bec10155f64f7{\npadding-bottom:0;\ncolor:#ffffff;\n}\nbody .av-special-heading.av-av_heading-730eb818ebc425e36f3bec10155f64f7 .av-special-heading-tag .heading-char{\nfont-size:25px;\n}\n.av-special-heading.av-av_heading-730eb818ebc425e36f3bec10155f64f7 .special-heading-inner-border{\nborder-color:#ffffff;\n}\n.av-special-heading.av-av_heading-730eb818ebc425e36f3bec10155f64f7 .av-subheading{\nfont-size:15px;\n}\n<\/style>\n<div  class='av-special-heading av-av_heading-730eb818ebc425e36f3bec10155f64f7 av-special-heading-h2 custom-color-heading blockquote modern-quote modern-centered  avia-builder-el-1  avia-builder-el-no-sibling '><h2 class='av-special-heading-tag'  itemprop=\"headline\"  >Une biologie, une physiopathologie et une th\u00e9rapie des cellules satellite du muscle squelettique<\/h2><div class=\"special-heading-border\"><div class=\"special-heading-inner-border\"><\/div><\/div><\/div>\n\n<\/div><\/div><\/main><!-- close content main element --><\/div><\/div><\/div><div id='av-layout-grid-1'  class='av-layout-grid-container av-av_layout_row-caf1f26e08707a2ebe9176b630e736c2 entry-content-wrapper main_color av-flex-cells  avia-builder-el-2  el_after_av_section  avia-builder-el-last  grid-row-not-first  container_wrap sidebar_right'  >\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-av_cell_three_fourth-5227a743201b625eadc00b27db60eab9\">\n.flex_cell.av-av_cell_three_fourth-5227a743201b625eadc00b27db60eab9{\nvertical-align:top;\n}\n.responsive #top #wrap_all .flex_cell.av-av_cell_three_fourth-5227a743201b625eadc00b27db60eab9{\npadding:30px 30px 30px 30px !important;\n}\n<\/style>\n<div class='flex_cell av-av_cell_three_fourth-5227a743201b625eadc00b27db60eab9 av-gridrow-cell av_three_fourth no_margin  avia-builder-el-3  el_before_av_cell_one_fourth  avia-builder-el-first ' ><div class='flex_cell_inner'><section  class='av_textblock_section av-av_textblock-0366cc7376be6c9e82a3e9cc8987b64f'  itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/CreativeWork\" ><div class='avia_textblock'  itemprop=\"text\" ><p style=\"text-align: center;\"><span style=\"font-weight: 400;\">Gr\u00e2ce \u00e0 beaucoup de personnes nous avons apport\u00e9 135.000 \u20ac \u00e0 cette ligne de recherche.<\/span><\/p>\n<\/div><\/section><br \/>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-av_hr-a6de236e6c183bbbd700292deacd2b52\">\n#top .hr.hr-invisible.av-av_hr-a6de236e6c183bbbd700292deacd2b52{\nheight:20px;\n}\n<\/style>\n<div  class='hr av-av_hr-a6de236e6c183bbbd700292deacd2b52 hr-invisible  avia-builder-el-5  el_after_av_textblock  el_before_av_textblock '><span class='hr-inner '><span class=\"hr-inner-style\"><\/span><\/span><\/div><br \/>\n<section  class='av_textblock_section av-av_textblock-0366cc7376be6c9e82a3e9cc8987b64f'  itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/CreativeWork\" ><div class='avia_textblock'  itemprop=\"text\" ><p><span style=\"font-weight: 400;\">Il s&rsquo;agit d&rsquo;un projet dirig\u00e9 vers le d\u00e9veloppement de nouvelles th\u00e9rapies pour la dystrophie Musculaire de Duchenne qui r\u00e9alise deux groupes de recherche \u00e0 Valence\u00a0:<\/span><\/p>\n<ul>\n<li style=\"font-weight: 400;\"><span style=\"font-weight: 400;\">D&rsquo;une part l&rsquo;\u00e9quipe du Dr. Palau du Centre de Recherche Pr\u00edncipe Felipe s&rsquo;est concentr\u00e9 sur l&rsquo;\u00e9tude de la biologie et de marqueurs des cellules satellites qui se chargent de r\u00e9g\u00e9n\u00e9rer le muscle endommag\u00e9 et son r\u00f4le peut \u00eatre tr\u00e8s important pour mettre au point de nouvelles th\u00e9rapies dans la maladie de Duchenne et d&rsquo;autres dystrophies. Au del\u00e0 de son acquisition, ils ont d\u00e9couvert une prot\u00e9ine ANKK1 qui peut \u00eatre cl\u00e9 pour l&rsquo;activation des cellules satellites et la diff\u00e9renciation des cellules musculaires.<\/span><\/li>\n<\/ul>\n<ul>\n<li style=\"font-weight: 400;\"><span style=\"font-weight: 400;\">L&rsquo;\u00e9quipe du Dr. V\u00edlchez de l&rsquo;H\u00f4pital Universitaire La Fe r\u00e9alise des essais cliniques avec diff\u00e9rentes th\u00e9rapies g\u00e9niques: bien en employant oligonucl\u00e9otides capables de produire des sauts d\u2019exons<\/span> <span style=\"font-weight: 400;\">pour restaurer la dystrophie, ou bien en provoquant des changements en employant le m\u00e9dicament Atalurano. Toutefois, dans son laboratoire il exp\u00e9rimente une nouvelle mol\u00e9cule appel\u00e9e PPRH qui est une alternative aux oligonucl\u00e9otides avec quelques prix plus accessibles.<\/span><\/li>\n<\/ul>\n<\/div><\/section><br \/>\n\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-av_image-f064293359dbd779858d0778dcf2fc1e\">\n.avia-image-container.av-av_image-f064293359dbd779858d0778dcf2fc1e img.avia_image{\nbox-shadow:none;\n}\n.avia-image-container.av-av_image-f064293359dbd779858d0778dcf2fc1e .av-image-caption-overlay-center{\ncolor:#ffffff;\n}\n<\/style>\n<div  class='avia-image-container av-av_image-f064293359dbd779858d0778dcf2fc1e av-styling- avia-align-center  avia-builder-el-7  el_after_av_textblock  el_before_av_textblock '   itemprop=\"image\" itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/ImageObject\" ><div class=\"avia-image-container-inner\"><div class=\"avia-image-overlay-wrap\"><img decoding=\"async\" class='wp-image-16373 avia-img-lazy-loading-not-16373 avia_image ' src=\"https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Captura-de-pantalla-2015-05-26-a-las-17.04.18.png\" alt='' title='Expresi\u00f3n y localizaci\u00f3n del marcador ANKK1'  height=\"378\" width=\"525\"  itemprop=\"thumbnailUrl\" srcset=\"https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Captura-de-pantalla-2015-05-26-a-las-17.04.18.png 525w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Captura-de-pantalla-2015-05-26-a-las-17.04.18-300x216.png 300w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Captura-de-pantalla-2015-05-26-a-las-17.04.18-450x324.png 450w\" sizes=\"(max-width: 525px) 100vw, 525px\" \/><\/div><\/div><\/div><br \/>\n<section  class='av_textblock_section av-av_textblock-0366cc7376be6c9e82a3e9cc8987b64f'  itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/CreativeWork\" ><div class='avia_textblock'  itemprop=\"text\" ><p><span style=\"font-weight: 400;\">La Fondation Isabelle Gemio finance les contrats de deux chercheurs: Estrella Rubio (marqueurs de cellules satellites) et Clara Gomis (sauts d&rsquo;exons avec PPRH).<\/span><\/p>\n<\/div><\/section><br \/>\n<div  class='avia-testimonial-wrapper av-av_testimonials-dfdcbe2bbda75220796248d01d289b52 avia-grid-testimonials avia-grid-1-testimonials avia_animate_when_almost_visible' >\n<section class=\"avia-testimonial-row\"><div class='avia-testimonial av-av_testimonial_single-d416bf633ce81f342d029a077ec113ed avia-testimonial-row-1 avia-first-testimonial flex_column no_margin av_one_full'><div class='avia-testimonial_inner'  itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/CreativeWork\" ><div class='avia-testimonial-image'  itemprop=\"image\" ><img loading=\"lazy\" decoding=\"async\" width=\"180\" height=\"180\" src=\"https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/JJVilchez1-180x180.jpg\" class=\"attachment-square size-square\" alt=\"Dr. Juan Vilchez Padilla\" srcset=\"https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/JJVilchez1-180x180.jpg 180w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/JJVilchez1-80x80.jpg 80w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/JJVilchez1-300x300.jpg 300w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/JJVilchez1-36x36.jpg 36w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/JJVilchez1-120x120.jpg 120w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/JJVilchez1-450x450.jpg 450w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/JJVilchez1.jpg 675w\" sizes=\"auto, (max-width: 180px) 100vw, 180px\" \/><\/div><div class='avia-testimonial-content '><div class='avia-testimonial-markup-entry-content'  itemprop=\"text\" ><p><strong>Grupo de Investigaci\u00f3n:<\/strong> Patolog\u00eda Neuromuscular y Ataxias, IIS-La Fe<\/p>\n<\/div><\/div><div class=\"avia-testimonial-meta\"><div class=\"avia-testimonial-arrow-wrap\"><div class=\"avia-arrow\"><\/div><\/div><div class='avia-testimonial-meta-mini'  itemprop=\"author\" itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/Person\" ><strong  class='avia-testimonial-name'  itemprop=\"name\" >Dr. Juan Vilchez Padilla<\/strong><span  class='avia-testimonial-subtitle '  itemprop=\"jobTitle\" >Investigador Jefe<\/span><span class='hidden avia-testimonial-markup-link'  itemprop=\"url\" >http:\/\/www.fundacionisabelgemio.com\/sobre-la-fundacion\/dr-juan-vilchez-padilla\/<\/span><span class=\"avia-testimonial-subtitle-sep\">&ndash;<\/span><a class='aviablank avia-testimonial-link' href='http:\/\/www.fundacionisabelgemio.com\/sobre-la-fundacion\/dr-juan-vilchez-padilla\/' rel=\u2019noopener noreferrer\u2019>Mas informacion<\/a><\/div><\/div><\/div><\/div><\/section>\n<section class=\"avia-testimonial-row\"><div class='avia-testimonial av-av_testimonial_single-22d56929efba5c2ffbadbb8e59b6ddb3 avia-testimonial-row-2 avia-first-testimonial flex_column no_margin av_one_full'><div class='avia-testimonial_inner'  itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/CreativeWork\" ><div class='avia-testimonial-image'  itemprop=\"image\" ><img loading=\"lazy\" decoding=\"async\" width=\"180\" height=\"180\" src=\"https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Francesc-Palau-180x180.jpg\" class=\"attachment-square size-square\" alt=\"Dr. Francesc Palau Mart\u00ednez\" srcset=\"https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Francesc-Palau-180x180.jpg 180w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Francesc-Palau-80x80.jpg 80w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Francesc-Palau-36x36.jpg 36w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Francesc-Palau-120x120.jpg 120w, https:\/\/www.fundacionisabelgemio.com\/wp-content\/uploads\/2015\/05\/Francesc-Palau.jpg 220w\" sizes=\"auto, (max-width: 180px) 100vw, 180px\" \/><\/div><div class='avia-testimonial-content '><div class='avia-testimonial-markup-entry-content'  itemprop=\"text\" ><p><strong>Grupo de Investigaci\u00f3n:<\/strong> Programa de Enfermedades Raras y Gen\u00e9ticas, Centro de Investigaci\u00f3n Pr\u00edncipe Felipe<\/p>\n<\/div><\/div><div class=\"avia-testimonial-meta\"><div class=\"avia-testimonial-arrow-wrap\"><div class=\"avia-arrow\"><\/div><\/div><div class='avia-testimonial-meta-mini'  itemprop=\"author\" itemscope=\"itemscope\" itemtype=\"https:\/\/schema.org\/Person\" ><strong  class='avia-testimonial-name'  itemprop=\"name\" >Dr. Francesc Palau Mart\u00ednez<\/strong><span  class='avia-testimonial-subtitle '  itemprop=\"jobTitle\" >Investigador Jefe<\/span><span class='hidden avia-testimonial-markup-link'  itemprop=\"url\" >http:\/\/www.fundacionisabelgemio.com\/sobre-la-fundacion\/dr-francesc-palau-martinez\/<\/span><span class=\"avia-testimonial-subtitle-sep\">&ndash;<\/span><a class='aviablank avia-testimonial-link' href='http:\/\/www.fundacionisabelgemio.com\/sobre-la-fundacion\/dr-francesc-palau-martinez\/' rel=\u2019noopener noreferrer\u2019>Mas informacion<\/a><\/div><\/div><\/div><\/div><\/section>\n<\/div><\/p>\n<\/div><\/div>\n<style type=\"text\/css\" data-created_by=\"avia_inline_auto\" id=\"style-css-av-av_cell_one_fourth-5227a743201b625eadc00b27db60eab9\">\n.flex_cell.av-av_cell_one_fourth-5227a743201b625eadc00b27db60eab9{\nvertical-align:top;\n}\n.responsive #top #wrap_all .flex_cell.av-av_cell_one_fourth-5227a743201b625eadc00b27db60eab9{\npadding:30px 30px 30px 30px !important;\n}\n<\/style>\n<div class='flex_cell av-av_cell_one_fourth-5227a743201b625eadc00b27db60eab9 av-gridrow-cell av_one_fourth no_margin  avia-builder-el-10  el_after_av_cell_three_fourth  avia-builder-el-last ' ><div 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